Another Look at PCSM-TCL

A small case series shows occurrence in children and supports its classification as a low-grade lymphoma.

Primary cutaneous CD4⁺ small/medium-sized pleomorphic T-cell lymphoma (PCSM-TCL) was provisionally included in the World Health Organization–European Organization for Research and Treatment of Cancer (WHO-EORTC) lymphoma classification of 2005. The umbrella term described disease characterized by dermal infiltrates of small- to medium-sized T cells without clinical or pathological evidence of mycosis fungoides.

This review of 10 cases identified in one tertiary academic center includes the youngest patient (age, 6 years) reported in the literature. Most of these patients (4 pediatric [age range, 6 to 16 years]; median age, 38 years; male:female ratio, 3:2) presented with a single papule, nodule, or plaque on the proximal trunk, head, or neck…

Reviewing Author

Angelica Selim, MD

Disclosures

Grant / Research support NIH/NCI, The Plastic Surgery Foundation

Angelica Selim, MD

Disclosures

Grant / Research support NIH/NCI, The Plastic Surgery Foundation

Another Look at PCSM-TCL

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Reviewing Author