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In this mixed prospective and retrospective study, the authors catalog the signs, symptoms, and clinical course of neuralgic amyotrophy in 246 patients who had been clinically diagnosed with idiopathic disease (199) or hereditary disease (47).
The main analysis excluded 43 patients treated with prednisone. Severe neuropathic pain was reported in 96.3% of cases and sensory involvement in 78.4%. Weakness was patchy, with a predilection for the upper and middle trunks in general and the long thoracic and suprascapular nerves (71.1%) in particular. Attacks recurred in 74.5% of those with hereditary disease and in 26.1% of those with idiopathic disease. Patients with hereditary disease had an earlier age at onset (28.4 vs. 41.3 years), more attac…