Loading...
The term "hair collar" refers to a ring of long, coarse hair surrounding cutaneous heterotopic brain tissue. This unusual pattern of hair growth is a marker for neural tube closure defects. These authors describe the cases of four children with the hair-collar sign associated with congenital midline exophytic scalp nodules.
All 4 infants had port-wine stains overlying the nodules and whorls of dark, coarse hair surrounding them. In 3 patients, MRI and/or surgical excision revealed encephaloceles (congenital scalp herniations through the cranium containing meningeal and brain tissue). One child had heterotopic brain tissue (brain tissue in the scalp without an underlying cranial defect). One patient with a parietal encephalocele also had agen…